Gorlin-Goltz Syndrome: Report of 4 Cases
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Published
Nov 7, 2020
Page:
47-54
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Ouassime Kerdoud
Department of Stomatology, Oral and Maxillofacial Surgery, Hospital of August 20th, University Hospital, Casablanca, Morocco.
Faical Slimani
Department of Stomatology, Oral and Maxillofacial Surgery, Hospital of August 20th, University Hospital, Casablanca, Morocco. and Faculty of Medicine and Pharmacy, Hassan 2 University of Casablanca, Casablanca, Morocco.
Abstract
Gorlin-Goltz syndrome, also known as basal cell nevomatosis (CBN), is a rare inherited disorder belonging to the family of neurocristopathies or diseases caused by abnormalities of the neural ridges. We report the case of 4 patients, suffering from this syndrome, followed up in the stomatology and maxillofacial surgery service in Casablanca, including a familial form in two cases: a mother and her son and 2 isolated cases, followed and treated in our service of maxillofacial surgery of the August 20 hospital in Casablanca. A clinical, biological and radiological assessment was made followed by surgical treatment for the 3 patients, an anatomo-pathological examination and the establishment of a strict monitoring plan.
Keywords:
Gorlin-Goltz syndrome, cell nevomatosis, stomatology, maxillofacial surgery.
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References
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Omrani H, et al. Recurrent ovarian fibromas in condition of gorlin syndrome; Journal de Gyn´ecologie Obst´etrique et Biologie de la Reproduction. 2010;39:584-587.
Kadlub N, et al. Pediatric keratocystic odontogenic tumor and nevoid basal cell carcinoma syndrome. Predictive factors for recurrence and aggressiveness: Rev Stomatol Chir Maxillofac. 2012;113:148-154.
Manfredi M, et al. Nevoid basal cell carcinoma syndrome: A review of the literature. Int. J. Oral. Maxillofac. Surg. 2004;33:117–124.
Dereure O. Gorlin syndrome and SUFU germline mutations: Annales de dermatologie et de vénéréologie. 2015; 142:231-232.
Mouhsine, et al. Syndrome de nævomatose baso-cellulaire: A propos de 2 cas, feuillets de radiologie. 2009;49(2): 111-115.
Salmon B, et al. Odontogenic keratocyst related to a Gorlin syndrome: A case report Archives de Pe´diatrie. 2008;15: 406-409.
Lo Muzio I. Gorlin syndrome. Encyclopédie Orphanet, Janvier; 2002.
Lomuzziol. Nevoid basal cell carcinoma syndrome (Gorlin syndrome). Orphanet Journal of Rare Diseases. 2008;3(32).
Kimonis VE, et al. Clinical manifestations in 105 persons with nevoid basal cell carcinoma syndrome. Am. J. Med. Genet. 1997;69: 229-308.
Omrani H, et al. Recurrent ovarian fibromas in condition of gorlin syndrome; Journal de Gyn´ecologie Obst´etrique et Biologie de la Reproduction. 2010;39:584-587.
Kadlub N, et al. Pediatric keratocystic odontogenic tumor and nevoid basal cell carcinoma syndrome. Predictive factors for recurrence and aggressiveness: Rev Stomatol Chir Maxillofac. 2012;113:148-154.