Gorlin-Goltz Syndrome: Report of 4 Cases

Main Article Content

Ouassime Kerdoud
Faical Slimani

Abstract

Gorlin-Goltz syndrome, also known as basal cell nevomatosis (CBN), is a rare inherited disorder belonging to the family of neurocristopathies or diseases caused by abnormalities of the neural ridges. We report the case of 4 patients, suffering from this syndrome, followed up in the stomatology and maxillofacial surgery service in Casablanca, including a familial form in two cases: a mother and her son and 2 isolated cases, followed and treated in our service of maxillofacial surgery of the August 20 hospital in Casablanca.  A clinical, biological and radiological assessment was made followed by surgical treatment for the 3 patients, an anatomo-pathological examination and the establishment of a strict monitoring plan.

Keywords:
Gorlin-Goltz syndrome, cell nevomatosis, stomatology, maxillofacial surgery.

Article Details

How to Cite
Kerdoud, O., & Slimani, F. (2020). Gorlin-Goltz Syndrome: Report of 4 Cases. Asian Journal of Dental Sciences, 3(4), 47-54. Retrieved from https://journalajds.com/index.php/AJDS/article/view/30129
Section
Case Study

References

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